The Prune-belly syndrome is the most common term for congenital absence, deficiency or hypoplasia of the abdominal musculature accompained by a large hypotonic bladder, dilated and tortuous ureters and bilateral cryptochidism.
This full-blom syndrome, which was associated with alobar holosencephaly with hydrocephalus, hypoplasia of lung and libs, markedly dilated cyst with hypertrophied muscular layer, mild hydroureter, polycystic kidney, colon atresia, agenesis of
pancreas,
spleen and genital organ and equinovalgus and genuvalgus, has been carefully observed in accordance with review of references.
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